{"id":3123,"date":"2014-12-11T11:55:55","date_gmt":"2014-12-11T11:55:55","guid":{"rendered":"http:\/\/old.institutcataladelpeu.com\/ca\/?p=3123"},"modified":"2016-10-21T08:52:24","modified_gmt":"2016-10-21T08:52:24","slug":"conceptes-generals-de-la-vasculitis","status":"publish","type":"post","link":"https:\/\/old.institutcataladelpeu.com\/ca\/conceptes-generals-de-la-vasculitis\/","title":{"rendered":"Conceptes generals de la vasculitis"},"content":{"rendered":"<div style=\"text-align: justify;\">\n<p style=\"text-align: justify;\"><span style=\"color: #000000;\"><span style=\"font-size: medium;\">La vasculitis agrupa totes les malalties o s\u00edndromes poc comunes amb un denominador com\u00fa, la inflamaci\u00f3 de qualsevol dels vasos sanguinis que disminueix parcialment o totalment el flux vascular.<\/span><\/span><\/p>\n<p>La causa sol ser per inflamaci\u00f3 motivada per afectaci\u00f3 immunit\u00e0ria o per invasi\u00f3 directa de les parets vasculars per agents pat\u00f2gens (v\u00edrics, mic\u00f2tics o bacterians). La vasculitis pot anar lligada a malalties reum\u00e0tiques com el lupus eritemat\u00f3s sist\u00e8mic o l&#8217;artritis reumatoide. Cursa amb febre, mi\u00e0lgies, artr\u00e0lgies, malestar general, infart visceral per isqu\u00e8mia, p\u00e8rdua de pes, m\u00e0cules vermelloses cut\u00e0nies (p\u00farpures) i insufici\u00e8ncia respirat\u00f2ria o renal.<\/p>\n<p>Existeixen onze tipus de vasculitis en funci\u00f3 de la grand\u00e0ria i localitzaci\u00f3 dels vasos afectats aix\u00ed com de la mostra histol\u00f2gica mitjan\u00e7ant bi\u00f2psia.<\/p>\n<p>Es classifiquen segons:<\/p>\n<p>1. LA GRAND\u00c0RIA DELS VASOS AFECTATS:<\/p>\n<p>&#8211; Vasculitis de vasos grans (arteritis de c\u00e8l\u00b7lules gegants, arteritis de Takayasu, etc.)<\/p>\n<p>&#8211; Vasculitis de vasos mitjans (malaltia de Kawasaki, poliarteritis nodosa)<\/p>\n<p>&#8211; Vasculitis de vasos petits (com la crioglobulin\u00e8mia mixta o la S\u00edndrome de Beh\u00e7et). Aquestes tenen el seu origen en dos grups:<\/p>\n<ul style=\"text-align: justify;\">\n<li><span style=\"color: #000000;\"><span style=\"font-size: medium;\">Per ANCA (anticossos citoplasm\u00e0tics antineutr\u00f2fils), com la gramulomatosi de Wegener, la S\u00edndrome de Churg-Strauss i la poliange\u00eftis microsc\u00f2pica.<\/span><\/span><\/li>\n<li><span style=\"color: #000000;\"><span style=\"font-size: medium;\">Per immunocomplexos com la vasculitis leucocitocl\u00e0stica cut\u00e0nia, la S\u00edndrome de Sch\u00f6nlein-Henoch, la S\u00edndrome Googpasture, etc.<\/span><\/span><\/li>\n<\/ul>\n<p style=\"text-align: justify;\"><span style=\"color: #000000;\"><span style=\"font-size: medium;\"><br \/>\n2. PRIMARIS O SECUNDARIS<\/span><\/span><\/p>\n<p>3. SOBRE LA BASE DELS MECANISMES PATOG\u00c8NICS.<\/p>\n<p>Es diagnostica mitjan\u00e7ant l&#8217;examen f\u00edsic, bi\u00f2psia, angiograma i an\u00e0lisi sangu\u00ednia.<\/p>\n<p>El tractament d&#8217;elecci\u00f3 s\u00f3n els glucocorticoides (prednisona) o esteroides. La dosi i durada dependr\u00e0 de la gravetat del tractament. Es poden utilitzar altres medicaments immunosupressors amb menys efectes secundaris que els glucocorticoides tals com la ciclofosfamida, metotrexat, azatioprina, etc.<\/p>\n<p>En conclusi\u00f3, davant un pacient amb sospita cl\u00ednica de vasculitis cut\u00e0nia, el primer que hem de fer \u00e9s confirmar el diagn\u00f2stic mitjan\u00e7ant l&#8217;examen cl\u00ednic, estudi anal\u00edtic, bi\u00f2psia o estudi radiol\u00f2gic (descartant la causa infecciosa). Confirmat el diagn\u00f2stic, cal establir el patr\u00f3 i l&#8217;extensi\u00f3 de la malaltia, arran de la qual, podrem classificar-la i tractar-la dins d&#8217;una s\u00edndrome prim\u00e0ria (arteritis temporal, gramulomatosi de Wegener, S\u00edndrome de Chung-Strauss), o b\u00e9 determinar com \u00e9s l&#8217;agent desencadenant. Aquest agent pot ser un antigen exogen o una malaltia subjacent que, en qualsevol cas, haurem de tractar m\u00e9s espec\u00edficament.<\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-1.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2108\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-1.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"768\" height=\"576\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/Vasculitis-2.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2109\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/Vasculitis-2.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"552\" height=\"694\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-3.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2110\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-3.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"516\" height=\"697\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-4.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2111\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-4.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"796\" height=\"591\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-5.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2112\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-5.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"736\" height=\"649\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-6.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2113\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-6.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"710\" height=\"947\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-7.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2114\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-7.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"768\" height=\"576\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-8.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2115\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-8.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"768\" height=\"576\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-9.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2116\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-9.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"704\" height=\"528\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-10.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2117\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-10.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"768\" height=\"576\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-11.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2118\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-11.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"768\" height=\"576\" \/><\/a><\/p>\n<p><a href=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-12.jpg\"><img  title=\"Conceptes generals de la vasculitis\" loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-2119\" src=\"http:\/\/old.institutcataladelpeu.com\/wp-content\/uploads\/2014\/12\/vasculitis-12.jpg\"  alt=\"Conceptes generals de la vasculitis\"  width=\"768\" height=\"576\" \/><\/a><\/p>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>La vasculitis agrupa totes les malalties o s\u00edndromes poc comunes amb un denominador com\u00fa, la inflamaci\u00f3 de qualsevol dels vasos sanguinis que disminueix parcialment o totalment el flux vascular. La causa sol ser per inflamaci\u00f3 motivada per afectaci\u00f3 immunit\u00e0ria o per invasi\u00f3 directa de les parets vasculars per agents pat\u00f2gens (v\u00edrics, mic\u00f2tics o bacterians). La [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":4616,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[276,306],"tags":[],"class_list":["post-3123","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-alteracions-dermatologiques","category-patologia-ca"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Conceptes generals de la vasculitis - Institut Catal\u00e0 del Peu<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"ca_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Conceptes generals de la vasculitis - Institut Catal\u00e0 del Peu\" \/>\n<meta property=\"og:description\" content=\"La vasculitis agrupa totes les malalties o s\u00edndromes poc comunes amb un denominador com\u00fa, la inflamaci\u00f3 de qualsevol dels vasos sanguinis que disminueix parcialment o totalment el flux vascular. La causa sol ser per inflamaci\u00f3 motivada per afectaci\u00f3 immunit\u00e0ria o per invasi\u00f3 directa de les parets vasculars per agents pat\u00f2gens (v\u00edrics, mic\u00f2tics o bacterians). 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